{"id":25172,"date":"2025-07-21T17:02:55","date_gmt":"2025-07-21T15:02:55","guid":{"rendered":"https:\/\/hedgehogprogram.com\/knowledge-hub\/non-categorise\/syndrome-du-herisson-chancelant\/"},"modified":"2026-01-04T16:43:59","modified_gmt":"2026-01-04T15:43:59","slug":"syndrome-du-herisson-chancelant","status":"publish","type":"epkb_post_type_1","link":"https:\/\/vh2023vjmwd-0.hosting-space.nl\/fr\/knowledge-hub\/notions-de-base-en-sante-et-medecine-veterinaire\/syndrome-du-herisson-chancelant\/","title":{"rendered":"Syndrome du h\u00e9risson chancelant"},"content":{"rendered":"\n<h4 class=\"wp-block-heading\"><em>Comprendre l&rsquo;une des maladies neurologiques les plus graves affectant les h\u00e9rissons pygm\u00e9es africains<\/em><\/h4>\n\n<p>Le syndrome du h\u00e9risson chancelant (SHC) est une affection neurologique d\u00e9g\u00e9n\u00e9rative et progressive qui touche le syst\u00e8me nerveux central des h\u00e9rissons, et plus particuli\u00e8rement le h\u00e9risson pygm\u00e9e d&rsquo;Afrique (Atelerix albiventris). Cette maladie, d\u00e9vastatrice et finalement mortelle, reste pourtant largement m\u00e9connue, m\u00eame de certains v\u00e9t\u00e9rinaires peu familiers avec la physiologie et la pathologie des h\u00e9rissons. <\/p>\n\n<p>Cet article vise \u00e0 expliquer ce qu&rsquo;est le WHS, ses causes, son \u00e9volution et comment il doit (et ne doit pas) \u00eatre diagnostiqu\u00e9 et pris en charge.<\/p>\n\n<h4 class=\"wp-block-heading\">Qu\u2019est-ce que le syndrome du h\u00e9risson chancelant ?<\/h4>\n\n<p>Le syndrome du h\u00e9risson chancelant est une maladie neurod\u00e9g\u00e9n\u00e9rative qui affecte la substance blanche du cerveau et de la moelle \u00e9pini\u00e8re, entra\u00eenant une paralysie progressive et une perte de motricit\u00e9. Il tire son nom du \u00ab vacillement \u00bb caract\u00e9ristique qui en est souvent le premier signe visible : un manque de coordination, notamment au niveau des pattes post\u00e9rieures. <\/p>\n\n<p>\u00c0 mesure que la maladie progresse, le h\u00e9risson perd la capacit\u00e9 de se tenir debout, de marcher, de se pelotonner, de manger et, finalement, m\u00eame d&rsquo;avaler ou de respirer correctement. Le syndrome de WHS est toujours mortel et incurable. <\/p>\n\n<h4 class=\"wp-block-heading\">Quelles sont les causes du syndrome d&rsquo;hyperstimulation musculaire (SHM) ?<\/h4>\n\n<p>La cause exacte du syndrome de WHS demeure inconnue, mais on pense qu&rsquo;il est d&rsquo;origine g\u00e9n\u00e9tique. Des \u00e9tudes sugg\u00e8rent une composante h\u00e9r\u00e9ditaire, notamment chez les lign\u00e9es de h\u00e9rissons pr\u00e9sentant un fort degr\u00e9 de consanguinit\u00e9, un probl\u00e8me fr\u00e9quent chez les populations de h\u00e9rissons domestiques en raison de la faible diversit\u00e9 g\u00e9n\u00e9tique. <\/p>\n\n<p>Il n&rsquo;existe aucune preuve que le syndrome de WHS soit contagieux ou d\u00e9clench\u00e9 uniquement par des facteurs environnementaux. Cependant, ses sympt\u00f4mes peuvent ressembler \u00e0 ceux d&rsquo;autres maladies, c&rsquo;est pourquoi un diagnostic approfondi est essentiel. <\/p>\n\n<h4 class=\"wp-block-heading\">Que se passe-t-il dans le corps : d\u00e9g\u00e9n\u00e9rescence du cerveau et de la moelle \u00e9pini\u00e8re<\/h4>\n\n<p>Le syndrome de WHS affecte principalement le syst\u00e8me nerveux central (SNC), et plus particuli\u00e8rement la substance blanche, constitu\u00e9e de fibres nerveuses responsables de la transmission des signaux dans tout le corps. Les l\u00e9sions qui en r\u00e9sultent entra\u00eenent : <\/p>\n\n<ul class=\"wp-block-list\">\n<li>D\u00e9my\u00e9linisation (perte de la gaine de my\u00e9line qui isole les nerfs)<\/li>\n\n\n\n<li>D\u00e9g\u00e9n\u00e9rescence axonale (destruction des fibres nerveuses)<\/li>\n\n\n\n<li>Cicatrices gliales (formation de cellules de soutien non fonctionnelles qui remplacent les neurones morts)<\/li>\n<\/ul>\n\n<p>Ces modifications perturbent la capacit\u00e9 du cerveau et de la moelle \u00e9pini\u00e8re \u00e0 envoyer des signaux moteurs coordonn\u00e9s, ce qui entra\u00eene une ataxie (perte de contr\u00f4le des mouvements corporels), une par\u00e9sie (faiblesse) et, finalement, une paralysie.<\/p>\n\n<p>L&rsquo;examen microscopique des tissus nerveux des h\u00e9rissons atteints, g\u00e9n\u00e9ralement post-mortem, r\u00e9v\u00e8le des l\u00e9sions bilat\u00e9rales et sym\u00e9triques, notamment au niveau du cervelet, du tronc c\u00e9r\u00e9bral et de la moelle \u00e9pini\u00e8re.<\/p>\n\n<h3 class=\"wp-block-heading\">Sympt\u00f4mes et \u00e9volution<\/h3>\n\n<p>Le syndrome WHS appara\u00eet g\u00e9n\u00e9ralement chez les h\u00e9rissons \u00e2g\u00e9s de 2 mois \u00e0 3 ans, bien que son apparition apr\u00e8s l&rsquo;\u00e2ge de 3 ans soit rare.<\/p>\n\n<p><strong>Premiers sympt\u00f4mes :<\/strong><\/p>\n\n<ul class=\"wp-block-list\">\n<li>L\u00e9g\u00e8re instabilit\u00e9 \u00e0 la marche, surtout au niveau des pattes arri\u00e8re<\/li>\n\n\n\n<li>L\u00e9g\u00e8re faiblesse ou tra\u00eenement du pied<\/li>\n\n\n\n<li>Tr\u00e9buchements ou chutes occasionnels<\/li>\n\n\n\n<li>Difficult\u00e9 \u00e0 garder l&rsquo;\u00e9quilibre en position debout immobile<\/li>\n<\/ul>\n\n<p><strong>Progression:<\/strong><\/p>\n\n<ul class=\"wp-block-list\">\n<li>Aggravation de l&rsquo;ataxie (mouvements incoordonn\u00e9s)<\/li>\n\n\n\n<li>Incapacit\u00e9 \u00e0 grimper ou \u00e0 se d\u00e9placer en fauteuil roulant<\/li>\n\n\n\n<li>Paralysie totale ou partielle des membres post\u00e9rieurs<\/li>\n\n\n\n<li>Atteinte ult\u00e9rieure des membres ant\u00e9rieurs et de la t\u00eate<\/li>\n\n\n\n<li>Difficult\u00e9s \u00e0 avaler et \u00e0 manger<\/li>\n\n\n\n<li>Tremblements ou spasmes musculaires semblables \u00e0 des crises d&rsquo;\u00e9pilepsie<\/li>\n\n\n\n<li>Perte de poids due \u00e0 l&rsquo;incapacit\u00e9 de manger ou de bouger<\/li>\n<\/ul>\n\n<p><strong>Stade avanc\u00e9 :<\/strong><\/p>\n\n<ul class=\"wp-block-list\">\n<li>Perte totale de la mobilit\u00e9 volontaire<\/li>\n\n\n\n<li>Atrophie musculaire<\/li>\n\n\n\n<li>Insuffisance respiratoire<\/li>\n\n\n\n<li>D\u00e9c\u00e8s ou euthanasie humanitaire en raison d&rsquo;une d\u00e9gradation de la qualit\u00e9 de vie<\/li>\n<\/ul>\n\n<p>La progression peut varier d&rsquo;une personne \u00e0 l&rsquo;autre, de quelques semaines \u00e0 plus d&rsquo;un an, mais le r\u00e9sultat final est toujours le m\u00eame.<\/p>\n\n<script async=\"\" src=\"https:\/\/pagead2.googlesyndication.com\/pagead\/js\/adsbygoogle.js?client=ca-pub-5480553163485780\" crossorigin=\"anonymous\"><\/script><!-- default --><ins class=\"adsbygoogle\" style=\"display:block\" data-ad-client=\"ca-pub-5480553163485780\" data-ad-slot=\"2364274238\" data-ad-format=\"auto\" data-full-width-responsive=\"true\"><\/ins><script>(adsbygoogle = window.adsbygoogle || []).push({});\n<\/script>\n\n<h4 class=\"wp-block-heading\">Attention : Erreurs de diagnostic fr\u00e9quentes<\/h4>\n\n<p>De nombreux h\u00e9rissons sont diagnostiqu\u00e9s \u00e0 tort comme souffrant du syndrome de dysfonctionnement h\u00e9rissonneux (SDH), notamment par des v\u00e9t\u00e9rinaires insuffisamment form\u00e9s aux sp\u00e9cificit\u00e9s de l&rsquo;esp\u00e8ce. Le SDH \u00e9tant un diagnostic d&rsquo;exclusion (c&rsquo;est-\u00e0-dire qu&rsquo;il ne peut \u00eatre pos\u00e9 qu&rsquo;apr\u00e8s avoir \u00e9cart\u00e9 toutes les autres causes possibles), tirer des conclusions h\u00e2tives sans examens compl\u00e9mentaires est dangereux et contraire \u00e0 l&rsquo;\u00e9thique. <\/p>\n\n<p>Conditions pouvant imiter les probl\u00e8mes de sant\u00e9 et s\u00e9curit\u00e9 au travail :<\/p>\n\n<ul class=\"wp-block-list\">\n<li><strong>Hernie discale (IVDD)<\/strong><br\/>Cette affection se caract\u00e9rise par la hernie discale, c&rsquo;est-\u00e0-dire la compression de la moelle \u00e9pini\u00e8re par un disque intervert\u00e9bral. Les sympt\u00f4mes peuvent ressembler \u00e0 ceux du syndrome de Wolff-Hirschhorn (WHS), mais le traitement peut inclure des cortico\u00efdes, le repos en cage ou une intervention chirurgicale. <br\/><\/li>\n\n\n\n<li><strong>Traumatisme ou l\u00e9sion de la colonne vert\u00e9brale<\/strong><br\/>Les chutes, les mauvaises manipulations ou d&rsquo;autres blessures peuvent provoquer une faiblesse temporaire ou permanente des membres post\u00e9rieurs.<br\/><\/li>\n\n\n\n<li><strong>Tentative d&rsquo;hibernation ou torpeur<\/strong><br\/>Un h\u00e9risson expos\u00e9 au froid peut devenir immobile, chancelant ou l\u00e9thargique. Il ne s&rsquo;agit pas du syndrome d&rsquo;hypothermie maligne et ce ph\u00e9nom\u00e8ne peut \u00eatre r\u00e9versible en r\u00e9chauffant progressivement l&rsquo;animal. <br\/><\/li>\n\n\n\n<li><strong>Carences nutritionnelles<\/strong><br\/>Un manque de vitamines B, E ou de calcium peut provoquer des sympt\u00f4mes neuromusculaires.<br\/><\/li>\n\n\n\n<li><strong>Infections ou parasites<\/strong><br\/>Les infections bact\u00e9riennes, virales ou parasitaires (telles que Baylisascaris procyonis ou la toxoplasmose) peuvent provoquer des signes neurologiques.<br\/><\/li>\n\n\n\n<li><strong>Cancer ou tumeurs<\/strong><br\/>Les tumeurs de la moelle \u00e9pini\u00e8re peuvent provoquer une faiblesse ou une paralysie des membres post\u00e9rieurs.<\/li>\n<\/ul>\n\n<p>N\u2019acceptez jamais un diagnostic de WHS sans examen v\u00e9t\u00e9rinaire approfondi, comprenant :<\/p>\n\n<ul class=\"wp-block-list\">\n<li>Examen neurologique<\/li>\n\n\n\n<li>analyses de sang<\/li>\n\n\n\n<li>Imagerie (radiographies, IRM si disponible)<\/li>\n\n\n\n<li>Analyses f\u00e9cales<\/li>\n\n\n\n<li>revue de la temp\u00e9rature et de la nutrition<\/li>\n\n\n\n<li>Prise en compte des ant\u00e9c\u00e9dents de traumatisme<\/li>\n<\/ul>\n\n<h4 class=\"wp-block-heading\">Diagnostic<\/h4>\n\n<p>Le diagnostic d\u00e9finitif du syndrome de Wolfram ne peut \u00eatre \u00e9tabli qu&rsquo;apr\u00e8s le d\u00e9c\u00e8s, par examen histopathologique des tissus c\u00e9r\u00e9braux et m\u00e9dullaires. Toutefois, un diagnostic pr\u00e9somptif peut \u00eatre pos\u00e9 du vivant du patient si : <\/p>\n\n<ul class=\"wp-block-list\">\n<li>Les sympt\u00f4mes correspondent \u00e0 l&rsquo;\u00e9volution classique<\/li>\n\n\n\n<li>Toutes les autres causes ont \u00e9t\u00e9 \u00e9cart\u00e9es.<\/li>\n\n\n\n<li>Le h\u00e9risson provient d&rsquo;une lign\u00e9e connue pour \u00eatre infect\u00e9e par le WHS.<\/li>\n<\/ul>\n\n<p>Les v\u00e9t\u00e9rinaires doivent documenter toutes les \u00e9tapes entreprises pour \u00e9liminer d&rsquo;autres possibilit\u00e9s avant de sugg\u00e9rer le WHS.<\/p>\n\n<h4 class=\"wp-block-heading\">Existe-t-il un rem\u00e8de ou un traitement ?<\/h4>\n\n<p>Malheureusement, il n&rsquo;existe aucun traitement curatif pour le syndrome de Wolfram. Aucun m\u00e9dicament, compl\u00e9ment alimentaire ou th\u00e9rapie connu n&rsquo;a prouv\u00e9 son efficacit\u00e9 pour stopper ou inverser la maladie. Cependant, des soins de soutien peuvent am\u00e9liorer le confort et prolonger la qualit\u00e9 de vie.  <\/p>\n\n<ul class=\"wp-block-list\">\n<li>Veillez \u00e0 ce que le h\u00e9risson reste au chaud, hydrat\u00e9 et nourri.<\/li>\n\n\n\n<li>Offrez une literie confortable et un acc\u00e8s facile \u00e0 la nourriture et \u00e0 l&rsquo;eau.<\/li>\n\n\n\n<li>Aider \u00e0 nourrir si n\u00e9cessaire<\/li>\n\n\n\n<li>Pr\u00e9venez les escarres en retournant r\u00e9guli\u00e8rement l&rsquo;animal.<\/li>\n\n\n\n<li>Utilisez des analg\u00e9siques ou des anti-inflammatoires si n\u00e9cessaire (consultez votre v\u00e9t\u00e9rinaire).<\/li>\n<\/ul>\n\n<p>Aux stades avanc\u00e9s, l&rsquo;euthanasie pratiqu\u00e9e avec humanit\u00e9 est souvent l&rsquo;option la plus humaine pour pr\u00e9venir les souffrances.<\/p>\n\n<h4 class=\"wp-block-heading\">\u00e9levage responsable et pr\u00e9vention<\/h4>\n\n<p>\u00c9tant donn\u00e9 que le WHS est suspect\u00e9 d&rsquo;\u00eatre d&rsquo;origine g\u00e9n\u00e9tique, la meilleure solution \u00e0 long terme consiste en un d\u00e9pistage g\u00e9n\u00e9tique et des pratiques d&rsquo;\u00e9levage responsables. Cela comprend : <\/p>\n\n<ul class=\"wp-block-list\">\n<li>\u00c9viter la consanguinit\u00e9 ou l&rsquo;\u00e9levage de h\u00e9rissons de lign\u00e9e inconnue<\/li>\n\n\n\n<li>Ne pas faire reproduire les h\u00e9rissons qui d\u00e9veloppent des sympt\u00f4mes neurologiques<\/li>\n\n\n\n<li>Tenir des registres pr\u00e9cis des arbres g\u00e9n\u00e9alogiques et des cas connus<\/li>\n\n\n\n<li>Sensibiliser les \u00e9leveurs et les propri\u00e9taires aux risques li\u00e9s \u00e0 la sant\u00e9 et \u00e0 la s\u00e9curit\u00e9 au travail<\/li>\n<\/ul>\n\n<h4 class=\"wp-block-heading\">Conclusion<\/h4>\n\n<p>Le syndrome du h\u00e9risson chancelant est une maladie tragique et incurable, mais il ne faut jamais l&rsquo;utiliser comme explication g\u00e9n\u00e9rale pour tout h\u00e9risson qui marche bizarrement ou qui pr\u00e9sente des signes de maladie.<\/p>\n\n<p>Un diagnostic pr\u00e9cis, de bonnes pratiques d&rsquo;\u00e9levage et un esprit critique sont essentiels pour quiconque prend soin de ces animaux fragiles. Bien qu&rsquo;il n&rsquo;existe aucun traitement curatif, nous pouvons n\u00e9anmoins faire beaucoup pour soutenir les h\u00e9rissons atteints, r\u00e9duire les erreurs de diagnostic et pr\u00e9venir la maladie gr\u00e2ce \u00e0 une meilleure sensibilisation aux pratiques d&rsquo;\u00e9levage. <\/p>\n\n<script async=\"\" src=\"https:\/\/pagead2.googlesyndication.com\/pagead\/js\/adsbygoogle.js?client=ca-pub-5480553163485780\" crossorigin=\"anonymous\"><\/script><!-- default --><ins class=\"adsbygoogle\" style=\"display:block\" data-ad-client=\"ca-pub-5480553163485780\" data-ad-slot=\"2364274238\" data-ad-format=\"auto\" data-full-width-responsive=\"true\"><\/ins><script>(adsbygoogle = window.adsbygoogle || []).push({});\n<\/script>\n\n<p><\/p>\n","protected":false},"excerpt":{"rendered":"<p>Comprendre l&rsquo;une des maladies neurologiques les plus graves affectant les h\u00e9rissons pygm\u00e9es africains Le syndrome du h\u00e9risson chancelant (SHC) est une affection neurologique d\u00e9g\u00e9n\u00e9rative et progressive qui touche le syst\u00e8me nerveux central des h\u00e9rissons, et plus particuli\u00e8rement le h\u00e9risson pygm\u00e9e d&rsquo;Afrique (Atelerix albiventris). Cette maladie, d\u00e9vastatrice et finalement mortelle, reste pourtant largement m\u00e9connue, m\u00eame de [&hellip;]<\/p>\n","protected":false},"author":1,"featured_media":20943,"comment_status":"closed","ping_status":"closed","template":"","meta":{"_monsterinsights_skip_tracking":false,"_monsterinsights_sitenote_active":false,"_monsterinsights_sitenote_note":"","_monsterinsights_sitenote_category":0,"site-sidebar-layout":"default","site-content-layout":"","ast-site-content-layout":"default","site-content-style":"default","site-sidebar-style":"default","ast-global-header-display":"","ast-banner-title-visibility":"","ast-main-header-display":"","ast-hfb-above-header-display":"","ast-hfb-below-header-display":"","ast-hfb-mobile-header-display":"","site-post-title":"","ast-breadcrumbs-content":"","ast-featured-img":"","footer-sml-layout":"","ast-disable-related-posts":"","theme-transparent-header-meta":"","adv-header-id-meta":"","stick-header-meta":"","header-above-stick-meta":"","header-main-stick-meta":"","header-below-stick-meta":"","astra-migrate-meta-layouts":"default","ast-page-background-enabled":"default","ast-page-background-meta":{"desktop":{"background-color":"var(--ast-global-color-4)","background-image":"","background-repeat":"repeat","background-position":"center center","background-size":"auto","background-attachment":"scroll","background-type":"","background-media":"","overlay-type":"","overlay-color":"","overlay-opacity":"","overlay-gradient":""},"tablet":{"background-color":"","background-image":"","background-repeat":"repeat","background-position":"center center","background-size":"auto","background-attachment":"scroll","background-type":"","background-media":"","overlay-type":"","overlay-color":"","overlay-opacity":"","overlay-gradient":""},"mobile":{"background-color":"","background-image":"","background-repeat":"repeat","background-position":"center center","background-size":"auto","background-attachment":"scroll","background-type":"","background-media":"","overlay-type":"","overlay-color":"","overlay-opacity":"","overlay-gradient":""}},"ast-content-background-meta":{"desktop":{"background-color":"var(--ast-global-color-5)","background-image":"","background-repeat":"repeat","background-position":"center center","background-size":"auto","background-attachment":"scroll","background-type":"","background-media":"","overlay-type":"","overlay-color":"","overlay-opacity":"","overlay-gradient":""},"tablet":{"background-color":"var(--ast-global-color-5)","background-image":"","background-repeat":"repeat","background-position":"center center","background-size":"auto","background-attachment":"scroll","background-type":"","background-media":"","overlay-type":"","overlay-color":"","overlay-opacity":"","overlay-gradient":""},"mobile":{"background-color":"var(--ast-global-color-5)","background-image":"","background-repeat":"repeat","background-position":"center center","background-size":"auto","background-attachment":"scroll","background-type":"","background-media":"","overlay-type":"","overlay-color":"","overlay-opacity":"","overlay-gradient":""}},"footnotes":""},"epkb_post_type_1_category":[680],"epkb_post_type_1_tag":[],"class_list":["post-25172","epkb_post_type_1","type-epkb_post_type_1","status-publish","has-post-thumbnail","hentry","epkb_post_type_1_category-notions-de-base-en-sante-et-medecine-veterinaire"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v27.3 - https:\/\/yoast.com\/product\/yoast-seo-wordpress\/ -->\n<title>Syndrome du h\u00e9risson chancelant &#187; The Hedgehog Program<\/title>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/vh2023vjmwd-0.hosting-space.nl\/fr\/knowledge-hub\/notions-de-base-en-sante-et-medecine-veterinaire\/syndrome-du-herisson-chancelant\/\" \/>\n<meta property=\"og:locale\" content=\"fr_FR\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Syndrome du h\u00e9risson chancelant &#187; The Hedgehog Program\" \/>\n<meta property=\"og:description\" content=\"Comprendre l&rsquo;une des maladies neurologiques les plus graves affectant les h\u00e9rissons pygm\u00e9es africains Le syndrome du h\u00e9risson chancelant (SHC) est une affection neurologique d\u00e9g\u00e9n\u00e9rative et progressive qui touche le syst\u00e8me nerveux central des h\u00e9rissons, et plus particuli\u00e8rement le h\u00e9risson pygm\u00e9e d&rsquo;Afrique (Atelerix albiventris). 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